Hereditary Angioedema Type III
A form of hereditary angioedema that occurs in women and is precipitated or worsened by high ESTROGEN levels. It is associated with mutations in the gene for FACTOR XII that result in its increased activity.
Year introduced: 2010
Date introduced: July 6, 2009
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Tree Number(s): C14.907.079.500.500, C17.800.862.945.066.500.500, C20.543.480.904.066.500.500
MeSH Unique ID: D056828
Entry Terms:
- Estrogen-Sensitive Hereditary Angioedema
- Angioedema, Estrogen-Sensitive Hereditary
- Angioedemas, Estrogen-Sensitive Hereditary
- Estrogen Sensitive Hereditary Angioedema
- Estrogen-Sensitive Hereditary Angioedemas
- Hereditary Angioedema, Estrogen-Sensitive
- Hereditary Angioedemas, Estrogen-Sensitive
- Estrogen-Related HAE
- Estrogen Related HAE
- Estrogen-Related HAEs
- HAE, Estrogen-Related
- HAEs, Estrogen-Related
- Estrogen-Sensitive HAE
- Estrogen Sensitive HAE
- Estrogen-Sensitive HAEs
- HAE, Estrogen-Sensitive
- HAEs, Estrogen-Sensitive
- Angioedema, Hereditary, Type III
- HAE with Normal C1 Inhibitor Concentration and Function
- Angioneurotic Edema, Hereditary, with Normal C1 Inhibitor Concentration and Function
- Hereditary Angioedema with Normal C1 Inhibitor Activity
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