Bernard-Soulier Syndrome
A familial coagulation disorder characterized by a prolonged bleeding time, unusually large platelets, and impaired prothrombin consumption.
Year introduced: 1991(1986)
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Subheadings:
Tree Number(s): C15.378.100.100.080, C15.378.140.120, C15.378.463.080, C16.320.099.080
MeSH Unique ID: D001606
Entry Terms:
- Bernard Soulier Syndrome
- Syndrome, Bernard-Soulier
- Giant Platelet Syndrome
- Platelet Syndromes, Giant
- Syndrome, Giant Platelet
- Syndromes, Giant Platelet
- Deficiency of Platelet Glycoprotein 1b
- Platelet Glycoprotein 1b, Deficiency of
- Von Willebrand Factor Receptor Deficiency
- Glycoprotein Ib, Platelet, Deficiency Of
- Platelet Glycoprotein Ib Deficiency
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