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Diabetes mellitus, transient neonatal, 2(TNDM2)

MedGen UID:
372150
Concept ID:
C1835887
Disease or Syndrome
Synonyms: ABCC8-Related Transient Neonatal Diabetes Mellitus 2; TNDM2
SNOMED CT: TNDM2 (609580007); Diabetes mellitus, transient neonatal 2 (609580007)
 
Gene (location): ABCC8 (11p15.1)
 
Monarch Initiative: MONDO:0012480
OMIM®: 610374

Definition

Any transient neonatal diabetes mellitus in which the cause of the disease is a mutation in the ABCC8 gene. [from MONDO]

Clinical features

From HPO
Type 2 diabetes mellitus
MedGen UID:
41523
Concept ID:
C0011860
Disease or Syndrome
WFS1 spectrum disorder (WFS1-SD) comprises classic WFS1 spectrum disorder and nonclassic WFS1 spectrum disorder. Classic WFS1-SD, a progressive neurodegenerative disorder, is characterized by onset of diabetes mellitus and optic atrophy before age 16 years. Additional complications may include one or more of the following: variable hearing impairment / deafness, diabetes insipidus, neurologic abnormalities, neurogenic bladder, and psychiatric abnormalities. Nonclassic WFS1-SD is less common than classic WFS1-SD. Phenotypes that appear to be milder than classic WFS1-SD include: optic atrophy and hearing impairment; neonatal diabetes, profound congenital deafness, and cataracts; isolated diabetes mellitus; isolated congenital cataracts; and isolated congenital, slowly progressive, and low-frequency (<2000 Hz) sensorineural hearing loss.
Transitory neonatal diabetes mellitus
MedGen UID:
449530
Concept ID:
C0342273
Disease or Syndrome
Hyperglycemia in the first month of life due to a genetically determined defect in the structure, secretion and/or function of insulin that resolves spontaneously within nine months of onset.

Professional guidelines

PubMed

Du T, Xia Y, Sun C, Gong Z, Liang L, Gong Z, Wang R, Lu D, Zhang K, Yang Y, Sun Y, Sun M, Sun Y, Xiao B, Qiu W
Orphanet J Rare Dis 2024 Feb 16;19(1):75. doi: 10.1186/s13023-024-03070-8. PMID: 38365697Free PMC Article
Bonfanti R, Iafusco D, Rabbone I, Diedenhofen G, Bizzarri C, Patera PI, Reinstadler P, Costantino F, Calcaterra V, Iughetti L, Savastio S, Favia A, Cardella F, Lo Presti D, Girtler Y, Rabbiosi S, D'Annunzio G, Zanfardino A, Piscopo A, Casaburo F, Pintomalli L, Russo L, Grasso V, Minuto N, Mucciolo M, Novelli A, Marucci A, Piccini B, Toni S, Silvestri F, Carrera P, Rigamonti A, Frontino G, Trada M, Tinti D, Delvecchio M, Rapini N, Schiaffini R, Mammì C, Barbetti F; Diabetes Study Group of ISPED
Eur J Endocrinol 2021 Apr;184(4):575-585. doi: 10.1530/EJE-20-1030. PMID: 33606663
Mackay D, Bens S, Perez de Nanclares G, Siebert R, Temple IK
Eur J Hum Genet 2014 Sep;22(9) Epub 2014 Feb 26 doi: 10.1038/ejhg.2014.27. PMID: 24569603Free PMC Article

Recent clinical studies

Etiology

Li X, Xu A, Sheng H, Ting TH, Mao X, Huang X, Jiang M, Cheng J, Liu L
Pediatr Diabetes 2018 Mar;19(2):251-258. Epub 2017 Aug 8 doi: 10.1111/pedi.12560. PMID: 28791793
Blair HA, Keating GM
Drugs 2016 Mar;76(3):363-74. doi: 10.1007/s40265-016-0541-z. PMID: 26821280

Diagnosis

Li X, Xu A, Sheng H, Ting TH, Mao X, Huang X, Jiang M, Cheng J, Liu L
Pediatr Diabetes 2018 Mar;19(2):251-258. Epub 2017 Aug 8 doi: 10.1111/pedi.12560. PMID: 28791793

Therapy

Li X, Xu A, Sheng H, Ting TH, Mao X, Huang X, Jiang M, Cheng J, Liu L
Pediatr Diabetes 2018 Mar;19(2):251-258. Epub 2017 Aug 8 doi: 10.1111/pedi.12560. PMID: 28791793
Blair HA, Keating GM
Drugs 2016 Mar;76(3):363-74. doi: 10.1007/s40265-016-0541-z. PMID: 26821280

Prognosis

Li X, Xu A, Sheng H, Ting TH, Mao X, Huang X, Jiang M, Cheng J, Liu L
Pediatr Diabetes 2018 Mar;19(2):251-258. Epub 2017 Aug 8 doi: 10.1111/pedi.12560. PMID: 28791793

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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