Prophylactic pacemaker placement at first signs of conduction disease in Kearns-Sayre syndrome
- PMID: 30326976
- DOI: 10.1017/S1047951118001609
Prophylactic pacemaker placement at first signs of conduction disease in Kearns-Sayre syndrome
Abstract
Cardiac conduction disease affects patients with Kearns-Sayre syndrome. We report a young asymptomatic patient with Kearns-Sayre syndrome with abnormal conduction on electrocardiogram and Holter monitor, although not advanced atrioventricular block. She underwent prophylactic pacemaker placement, and rapidly developed complete atrioventricular block, which resulted in 100% ventricular pacing. It may be reasonable to consider prophylactic pacemaker implantation in patients with Kearns-Sayre syndrome with evidence of cardiac conduction disease even without overt atrioventricular block given its unpredictable progression to complete atrioventricular block.
Keywords: Kearns–Sayre syndrome; conduction; pacemaker; pediatrics.
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